用戶【Ïvÿ Ćhëñ】點評問題和點評內容

【評論主題】32.出生 7 天大嬰兒吐奶、吸奶無力,血液檢查 pH 值為 7.21,pCO2:24 torr,HCO3-:12 mEq/L,Na+:140 mEq/L,K+:5.6 mEq/L。尿液之 keton

【評論內容】

Phenyketouria :

-decrease metabolism of phenylalanine

-microcephaly, mental disorder, seizure

Medium chain acyl CoA dehydrogenase deficiency :

-inability to break down medium chain fatty acids into acetyl CoA

-hypoglycemia

Glutaric aciduria type I :

-unable to completely break down lysine, hydroxylysine and tryptophan

-macrocephaly, mental retardation

Isovaleric acidemia :

-disruption of normal metabolism of the branched chain amino acid leucine

-characterized by distinctive odor of sweaty feet

【評論主題】23.有關 Leukocyte adhesion deficiency 的敘述,下列何者正確?(A)為性聯遺傳 (B)常有臍帶感染、且合併臍帶較晚脫落之病史 (C)通常嗜中性白血球絕對值會下降 (D)

【評論內容】

Leukocyte adhesion deficiency

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- Autosomal recessive (A)

- Cause immunodeficiency resulting in recurrent infection

- defect in neutrophil adhesion--->poor leukocyte chemotaxis--->inability to form pus(D) and neutrophilia(C, not absolute neutrophil count)

**delay in umbilical cord sloughing**(B)

【評論主題】4.下列何種不是活性減毒疫苗?(A)卡介苗(BCG vaccine)(B)輪狀病毒疫苗(Rotavirus vaccine)(C)麻疹、腮腺炎、德國麻疹疫苗(MMR vaccine)(D)B型肝炎疫苗

【評論內容】

Memonic JR MV BOY

J - japanese encephalitis

R - rota

M - MMR

V - varicella

B - BCG

O - oral polio (Sabin)

Y - yellow fever

【評論主題】42.一名12歲45公斤重的男童,因為急性闌尾炎接受腹腔鏡闌尾切除手術,下列何者是比較適當的點滴輸液?(A)每24小時給與2,000毫升輸液,其中內含5%葡萄糖,0.45%氯化鈉,20毫當量/升(mE

【評論內容】

Body weight 45 kg

----------------------

First 10 kg      - 100ml/kg   - 1000ml

Second 20 kg- 50ml/kg     -    500ml

The rest         - 20ml/kg      -    500ml

Therefore total fluid need for 45 kg boy is 2000ml. 

As he need to undergo emergency operation, nothing by mouth is a must.

So, if we give only NaCl won't be enough for him, fluid with glucose and potassium is a good choice for this condition.

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