【評論主題】32.出生 7 天大嬰兒吐奶、吸奶無力,血液檢查 pH 值為 7.21,pCO2:24 torr,HCO3-:12 mEq/L,Na+:140 mEq/L,K+:5.6 mEq/L。尿液之 keton
【評論內容】
Phenyketouria :
-decrease metabolism of phenylalanine
-microcephaly, mental disorder, seizure
Medium chain acyl CoA dehydrogenase deficiency :
-inability to break down medium chain fatty acids into acetyl CoA
-hypoglycemia
Glutaric aciduria type I :
-unable to completely break down lysine, hydroxylysine and tryptophan
-macrocephaly, mental retardation
Isovaleric acidemia :
-disruption of normal metabolism of the branched chain amino acid leucine
-characterized by distinctive odor of sweaty feet
【評論主題】23.有關 Leukocyte adhesion deficiency 的敘述,下列何者正確?(A)為性聯遺傳 (B)常有臍帶感染、且合併臍帶較晚脫落之病史 (C)通常嗜中性白血球絕對值會下降 (D)
【評論內容】
Leukocyte adhesion deficiency
-----------------------------------
- Autosomal recessive (A)
- Cause immunodeficiency resulting in recurrent infection
- defect in neutrophil adhesion--->poor leukocyte chemotaxis--->inability to form pus(D) and neutrophilia(C, not absolute neutrophil count)
**delay in umbilical cord sloughing**(B)
【評論主題】4.下列何種不是活性減毒疫苗?(A)卡介苗(BCG vaccine)(B)輪狀病毒疫苗(Rotavirus vaccine)(C)麻疹、腮腺炎、德國麻疹疫苗(MMR vaccine)(D)B型肝炎疫苗
【評論內容】
Memonic JR MV BOY
J - japanese encephalitis
R - rota
M - MMR
V - varicella
B - BCG
O - oral polio (Sabin)
Y - yellow fever
【評論主題】36.一位36歲病人過去無特殊病史,最近發現頸部及腋下有多顆直徑1~3公分之淋巴結,腹股溝亦有數顆淋巴結,最大者直徑約4公分。頸部淋巴結切片診斷為B細胞瀰漫性大細胞淋巴瘤(diffuse large
【評論內容】Hodgkin's lymphoma-R☆ ☆☆☆☆☆ +-...
【評論主題】42.一名12歲45公斤重的男童,因為急性闌尾炎接受腹腔鏡闌尾切除手術,下列何者是比較適當的點滴輸液?(A)每24小時給與2,000毫升輸液,其中內含5%葡萄糖,0.45%氯化鈉,20毫當量/升(mE
【評論內容】
Body weight 45 kg
----------------------
First 10 kg - 100ml/kg - 1000ml
Second 20 kg- 50ml/kg - 500ml
The rest - 20ml/kg - 500ml
Therefore total fluid need for 45 kg boy is 2000ml.
As he need to undergo emergency operation, nothing by mouth is a must.
So, if we give only NaCl won't be enough for him, fluid with glucose and potassium is a good choice for this condition.
^^*